Single ventricle
Single ventricle is a rare congenital heart defect, which constitutes just over 1% of congenital cardiovascular diseases. The single functional ventricle could be morphologically right or left with the second ventricle usually hypoplastic and/or insufficiently functional. Therefore, there are several subtypes of the disease, depending on which ventricle is underdeveloped.
- Single ventricle with functional left ventricle:
- Pulmonal atresia
- Tricuspidal atresia
- Double inlet left ventricle
- Double outlet left ventricle
- Single ventricle with functional right ventricle:
- Hypoplastic left heart syndrome
- Double inlet right ventricle
- Double outlet right ventricle
- Single ventricle heterotaxy syndrome is also included to this category.