Hypoplastic right heart syndrome

Hypoplastic right heart syndrome
Diagram of a heart with underdeveloped right side (tricuspid, pulmonary valve, and right ventricle)
SpecialtyCardiology
DurationLifetime
Diagnostic methodFetal echocardiogram
TreatmentCardiac surgery
Frequency60,000 cases per year, US

Hypoplastic right heart syndrome (HRHS) is a congenital heart defect in which the structures on the right side of the heart, particularly the right ventricle, are underdeveloped. This defect causes inadequate blood flow to the lungs, and thus a cyanotic infant.